A case with dermatofibrosarcoma protuberans: Dermatofibrosarkom protuberans olgusu

Cenk Akçalı; Suna Erkılıç; Necmettin Kırtak; Neslihan Karslı; Hüseyin Serhat İnalöz

doi:10.5455/GMJ-30-41366

Authors

Cenk Akçalı University of Gaziantep, Faculty of Medicine, Department of Dermatology, Gaziantep
Suna Erkılıç University of Gaziantep, Faculty of Medicine, Department of Pathology, Gaziantep
Necmettin Kırtak University of Gaziantep, Faculty of Medicine, Department of Dermatology, Gaziantep
Neslihan Karslı University of Gaziantep, Faculty of Medicine, Department of Dermatology, Gaziantep
Hüseyin Serhat İnalöz University of Gaziantep, Faculty of Medicine, Department of Pathology, Gaziantep

DOI:

https://doi.org/10.5455/GMJ-30-41366

Keywords:

Dermatofibrosarcoma protuberans, sarcoma

Abstract

Dermatofibrosarcoma protuberans is a rare semi-malignant characterized tumor, derived from dermal fibroblasts, and mostly localized in the trunk. It is often seen in group of middle-age. It is characterized with one or more raised, hard, erythemathos, sometimes painful nodules. Over time, it turns to plaques, and can be ulcerated. A twenty-two-year-old male, with numerous asymptomatic papules above the right scapula, admitted to our clinic. The lesion had started as a small papule about two years ago, and the patient had used topical cortisone medications. With clinical and histopathological findings the present case was diagnosed as dermatofibrosarcoma protuberans. As a rare disease, the case was discussed in the light of literature.

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