Spinal anesthesia for a rare case of Proteus syndrome: Nadir görülen Proteus sendromlu olguda spinal anestezi

Mustafa  Özgür; Fatma Bilge Ceylan; Serkan  Özler

doi:10.5455/GMJ-30-156339

Authors

Mustafa Özgür Department of Anesthesiology and Reanimation, Antakya State Hospital, Hatay, Turkey
Fatma Bilge Ceylan Department of Anesthesiology and Reanimation, Antakya State Hospital, Hatay, Turkey
Serkan Özler Department of Urology, Antakya State Hospital, Hatay, Turkey

DOI:

https://doi.org/10.5455/GMJ-30-156339

Keywords:

Proteus syndrome, spinal anesthesia, urolithiasis

Abstract

Our purpose is to present an uneventful spinal anesthesia experience in a rare case with Proteus syndrome (PS) suffering from urolithiasis. A 17-year-old male patient with previously diagnosed PS admitted to the urology polyclinic for urolithiasis. Physical examination showed disproportionate growth of the lower extremities, amputated toes and superficial and large veins in the legs. Spinal anesthesia was successfully administered at sitting position through the intrathecal route via the L3-4 space in the midline. Since it also includes difficult airways, spinal canal deformities, thromboembolisms, and certain pathologies such as cystic abnormalities in the lung, emphysema, atelectasis and fibrosis, this syndrome should be considered further with respect to anesthesia. The most significant cause of mortality in PS is pulmonary thromboembolism induced by deep vein thrombosis caused by growing extremities. Spinal anesthesia has provided a more reliable method of anesthesia due to the lower risk of development of thromboembolism in this case.

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