Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis

Tuberosklerozla ilişkili renal anjiomiyolipomun sebep olduğu intraperitoneal kanamayı taklit eden akut retroperitoneal hematom


Abstract views: 23 / PDF downloads: 14

Authors

  • İlker Seçkiner Department of Urology, Faculty of Medicine, University of Gaziantep, Gaziantep
  • Aykut Altunkaya Department of Thorax Surgery, Bağcılar Education and Research Hospital, İstanbul
  • Ömer Bayrak Department of Urology, Faculty of Medicine, University of Gaziantep, Gaziantep
  • Bülent Akduman Department of Urology, Faculty of Medicine, Zonguldak Karaelmas University, Zonguldak
  • Aydın Mungan Department of Urology, Faculty of Medicine, Zonguldak Karaelmas University, Zonguldak

DOI:

https://doi.org/10.5455/GMJ-30-2012-72

Keywords:

Angiomyolipoma, hemorrhage, tuberous sclerosis

Abstract

Tuberous sclerosis complex (TSC) is known as a neurological and dermatological disorder, but its renal manifestations are frequent and may cause death. We report a patient with TSC who showed bilateral multiple renal angiomyolipomas. Spontaneous retroperitoneal hematoma caused by renal angiomyolipoma that mimicking intraperitoneal hemorrhage was diagnosed in her clinical follow-up. We performed right total nephrectomy for controlling hemorrhage, but she died due to poor respiratory function, in fifteenth day postoperatively.

Metrics

Metrics Loading ...

References

Young J, Povey S. The genetic basis of tuberous sclerosis. Mol Med Today 1998;4(7):313-9.

Van Baal JG, Smits NJ, Keeman JN, Lindhout D, Verhoef S. The evolution of renal angiomyolipomas in patients with tuberous sclerosis. J Urol 1994;152(1):35-8.

Oesterling JE, Fishman EK, Goldman SM, Marshall FF. The management of renal angiomyolipoma. J Urol 1986;135(6):1121-4.

Harabayashi T, Shinohara N, Katano H, Nonomura K, Shimizu T, Koyanagi T. Management of renal angiomyolipomas associated with tuberous sclerosis complex. J Urol 2004;171(1):102-5.

Kushwaha R, Dhawan I, Arora R, Gupta K, Dhupia JS. Multifocal renal angiomyolipoma presenting as massive intraabdominal hemorrhage. Indian J Pathol Microbiol 2010;53(2):340-1.

Granata A, Basile A, Figuera M, Mignani R, Fiore CE. Spontaneous retroperitoneal hemorrhage due to massive rupture of renal angiomyolipoma treated with nephrectomy: an unusual onset of tuberous sclerosis complex. Clin Nephrol 2009;71(4):441-4.

Tan BW, Toh KL. Life threatening intraperitoneal hemorrhage with abdominal compartment syndrome: unusual presentation of renal angiomyolipoma. Int J Urol 2010;17(9):820-1.

Shepherd CW, Gomez MR, Lie JT, Crowson CS. Causes of death in patients with tuberous sclerosis. Mayo Clin Proc 1991;66(8):792-6.

Downloads

Published

2023-05-02

How to Cite

Seçkiner, İlker, Altunkaya, A., Bayrak, Ömer, Akduman, B., & Mungan, A. (2023). Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis: Tuberosklerozla ilişkili renal anjiomiyolipomun sebep olduğu intraperitoneal kanamayı taklit eden akut retroperitoneal hematom. European Journal of Therapeutics, 18(2), 106–108. https://doi.org/10.5455/GMJ-30-2012-72

Issue

Section

Case Reports