Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis

Tuberosklerozla ilişkili renal anjiomiyolipomun sebep olduğu intraperitoneal kanamayı taklit eden akut retroperitoneal hematom


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Authors

  • İlker Seçkiner Department of Urology, Faculty of Medicine, University of Gaziantep, Gaziantep
  • Aykut Altunkaya Department of Thorax Surgery, Bağcılar Education and Research Hospital, İstanbul
  • Ömer Bayrak Department of Urology, Faculty of Medicine, University of Gaziantep, Gaziantep
  • Bülent Akduman Department of Urology, Faculty of Medicine, Zonguldak Karaelmas University, Zonguldak
  • Aydın Mungan Department of Urology, Faculty of Medicine, Zonguldak Karaelmas University, Zonguldak

DOI:

https://doi.org/10.5455/GMJ-30-2012-72

Keywords:

Angiomyolipoma, hemorrhage, tuberous sclerosis

Abstract

Tuberous sclerosis complex (TSC) is known as a neurological and dermatological disorder, but its renal manifestations are frequent and may cause death. We report a patient with TSC who showed bilateral multiple renal angiomyolipomas. Spontaneous retroperitoneal hematoma caused by renal angiomyolipoma that mimicking intraperitoneal hemorrhage was diagnosed in her clinical follow-up. We performed right total nephrectomy for controlling hemorrhage, but she died due to poor respiratory function, in fifteenth day postoperatively.

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References

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Granata A, Basile A, Figuera M, Mignani R, Fiore CE. Spontaneous retroperitoneal hemorrhage due to massive rupture of renal angiomyolipoma treated with nephrectomy: an unusual onset of tuberous sclerosis complex. Clin Nephrol 2009;71(4):441-4.

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Published

2023-05-02

How to Cite

Seçkiner, İlker, Altunkaya, A., Bayrak, Ömer, Akduman, B., & Mungan, A. (2023). Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis: Tuberosklerozla ilişkili renal anjiomiyolipomun sebep olduğu intraperitoneal kanamayı taklit eden akut retroperitoneal hematom. European Journal of Therapeutics, 18(2), 106–108. https://doi.org/10.5455/GMJ-30-2012-72

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Case Reports