Prevention of recurrence of stroke in a patient with sickle  cell disease who has Moyamoya Syndrome

Süheyl Asma; Can Boğa; Meliha Tan; Mutlu Kasar; Mahmut Yeral; Şerife Nur Ulusan

doi:10.5455/GMJ-30-2013-151

Authors

Süheyl Asma Baskent University Faculty of Medicine, Department of Family Medicine, Adana
Can Boğa Baskent University Faculty of Medicine, Department of Hematology, Adana
Meliha Tan Baskent University Faculty of Medicine, Department of Neurology, Adana
Mutlu Kasar Baskent University Faculty of Medicine, Department of Hematology, Adana
Mahmut Yeral Baskent University Faculty of Medicine, Department of Hematology, Adana
Şerife Nur Ulusan Baskent University Faculty of Medicine, Department of Radiology, Adana

DOI:

https://doi.org/10.5455/GMJ-30-2013-151

Keywords:

Moyamoya, sickle cell anemia, stroke, red cell exchange

Abstract

Moyamoya syndrome may occur several years after cerebrovascular event in patients with sickle cell disease. This manuscript presents the efforts to prevent recurrence of stroke by using hydroxyurea and red cell exchange therapy after developing early signs of a new neurological attack in a patient with Moyamoya syndrome.

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References

Dobson SR, Holden KR, Nietert PJ, Cure JK, Laver JH, Disco D, et al. Moyamoya syndrome in childhood sickle cell disease: a predictive factor for recurrent cerebrovascular events. Blood 2002;99(9):3144-50.

Kim JM, Lee SH, Roh JK. Changing ischaemic lesion patterns in adult moyamoya disease. J Neurol Neurosurg Psychiatry 2009;80(1):36-40.

Metcalfe SA, Barlow-Stewart K, Campbell J, Emery J. Genetics and blood-hemoglobinopathies and clotting disorders. Aust Fam Physician 2007;36(10):812-9.

Bhattacharyya M, Kannan M, Chaudhry VP, Mahapatra M, Pati H, Saxena R. Hypercoagulable state in five thalassemia intermedia patients. Clin Appl Thromb Hemost 2007;13(4):422-7.

Singh R, Venketesubramanian N. Recurrent cerebral infarction in beta thalassaemia major. Cerebrovasc Dis 2004;17(4):344-5.

Mukherje A. Moyamoya disease and beta-thalassemia. J Assoc Physicians India 1995;43(10):710-1.

Sanefuji M, Ohga S, Kira R, Yoshiura T, Torisu H, Hara T. Moyamoya syndrome in a splenectomized patient with betathalassemia intermedia. J Child Neurol 2006;21(1):75-7.

Owecki M, Wegrzyn D, Kozubski W. Ischemic manifestation of adult moyamoya disease: a case report. Neurol Neurochir Pol 2003;37(2):419-27.

Gorrotxategi P, Reguilón MJ, Gaztañaga R. Moya-moya disease in a child with multiple malformations. Rev Neurol 1995;23(120):403-5.