Vein of Galen Aneurysmal Malformation  Presenting with Macrocephaly

Hüseyin Gümüş; Halil Kazanasmaz; Mustafa  Çalık

doi:10.5152/EurJTher.2017.200

Authors

Hüseyin Gümüş Department of Pediatrics, Harran University School of Medicine https://orcid.org/0000-0002-9326-2194
Halil Kazanasmaz Department of Pediatrics, Harran University School of Medicine https://orcid.org/0000-0003-4671-4028
Mustafa Çalık Department of Pediatric Neurology, Harran University School of Medicine https://orcid.org/0000-0002-6383-3355

DOI:

https://doi.org/10.5152/EurJTher.2017.200

Keywords:

Vein of Galen malformation, macrocephaly, congenital

Abstract

The vein of Galen aneurysmal malformation (VGAM) is a rare congenital intracranial vascular malformation found in children. Dilatation of the vein of Galen is a common feature of VGAM. This malformation is actually a vascular lesion that may present as different clinical pictures in childhood and is difficult to extract using classical surgical methods because of its locality and hemodynamic structure. Major complications of VGAM include heart failure, hydrocephaly, intracranial bleeding, and vascular steal phenomenon. Here the case of a 4-year-old girl who presented with macrocephaly and was diagnosed with VGAM is discussed in the light of literature

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