Congenital Extrahepatic Portosystemic Shunt:  Abernethy Malformation Type 2

Mehmet Nur Kaya; Ömer Toprak; Sultan Türel; Uğur Ergün; Taha Yasin Arslan

doi:10.5152/EurJTher.2019.600

Authors

Mehmet Nur Kaya Department of Internal Medicine, Balıkesir University School of Medicine, Balıkesir https://orcid.org/0000-0003-4368-3078
Ömer Toprak Department of Nephrology, Balıkesir University School of Medicine, Balıkesir https://orcid.org/0000-0002-2865-1687
Sultan Türel Department of Internal Medicine, Balıkesir University School of Medicine, Balıkesir https://orcid.org/0000-0002-7073-6529
Uğur Ergün Department of Internal Medicine, Balıkesir University School of Medicine, Balıkesir https://orcid.org/0000-0002-6111-0030
Taha Yasin Arslan Department of Radiology, Balıkesir University School of Medicine, Balıkesir https://orcid.org/0000-0002-4116-0540

DOI:

https://doi.org/10.5152/EurJTher.2019.600

Keywords:

Abdominal pain, abernethy malformation, congenital anomaly

Abstract

Abernethy malformation is a vascular congenital anomaly in which extrahepatic portocaval shunts develop. The patient was admitted to the gastroenterology department with complaints of abdominal pain and nausea. Ammonia and bilirubin levels were increased in the laboratory values and other liver function values were normal. The shunt was detected between the inferior vena cava and portal vein by ultrasonography and computed tomography, and the portal vein was hypoplastic. In this case report, we present a male patient diagnosed with Abernethy malformation type 2.

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