Melkersson-Ronsenthal Syndrome

Muzaffer KANLIKAMA; Semih  MUMBUÇ; Tufan  YAKIT

doi:10.58600/eurjther.1997-8-1-2-1505-arch

Authors

Muzaffer KANLIKAMA Gaziantep Üniversitesi Tıp Fakültesi KBB Anabilim Dalı
Semih MUMBUÇ Gaziantep Üniversitesi Tıp Fakültesi KBB Anabilim Dalı
Tufan YAKIT Gaziantep Üniversitesi Tıp Fakültesi KBB Anabilim Dalı

DOI:

https://doi.org/10.58600/eurjther.1997-8-1-2-1505-arch

Keywords:

Melkersson-Rosenthal syndrome, facial paralysis, cheilitis

Abstract

Melkersson-Rosenthal Syndrome (MRS) is a rare condition that cause and pathogenesis is not known. Triad of syndrome are recurrent orofacial edema together with cheilitis of the lip, recurrent peripheral type facia[ nerve paralysis and fissural tongue. But complete triad is seen only one third of the patients. Most frequent and diagnostic symptom of the disease is orofacial edema. Disease affects young ages. Facia! nerve paralysis likes to Bell's palsy and tends to recur. Far treatment, conservative approach with steroids is preferred. If it recurs frequently, total facia! nerve decompression is suggested.

In this paper, two cases of MRS with complete triad were presented and clinical presentations and treatment of this syndrome were discussed.

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