Basal Cell Nevoid Syndrome

Semih  MUMBUÇ; Muzaffer  KANLIKAMA; Mustafa  SEĞMEN

doi:10.58600/eurjther.1997-8-1-2-1500-arch

Authors

Semih MUMBUÇ Gaziantep Üniversitesi Tıp Fakültesi KBB Anabilim Dalı
Muzaffer KANLIKAMA Gaziantep Üniversitesi Tıp Fakültesi KBB Anabilim Dalı
Mustafa SEĞMEN Gaziantep Üniversitesi Tıp Fakültesi KBB Anabilim Dalı

DOI:

https://doi.org/10.58600/eurjther.1997-8-1-2-1500-arch

Keywords:

Basal celi nevoid syndrome, odontogenic cysts

Abstract

Basal celi nevoid syndrome (BCNS) is a rare familial disease which shows characteristic facia! appearance, multiple nevuses or nevoid hasal celi carcinomas and skeletal anomalies. it has autosomal dominant trait.

In this article, two cases of BCNS from same family were presented and their clinical findings were discussed.

Metrics

Metrics Loading ...

References

Angelopoulou EK, Nikolatou O: Odonto genic keratocysts: Clinicopathologic study of 87 cases. J Oral Maxillofacial Surg 48: 593, 1990

Erannon RE: The odontogenic keratocyst. a clinicopathologic study of 312 cases. part 1: clinical features. Oral Surg Oral Med Oral Pathol 42:54, 1976

Erowne RM: The odontogenic keratocyst; clinical aspects. Er Dent J 128: 225, 1970

Forssell K, Forssell H, Kahnherg KE: Recurrence of keratocysts. a long term follow up study. lnt J Oral Maxillofac Surg 17: 25, 1988

Gorlin RJ, Goltz RW: Multiple nevoid hasal cell epithelioma jaw cysts and hifid rih. New Eng J Med 262: 908, 1960

Gorlin RJ: Nevoid hasal cell carsinoma syndrome. Medicine 66: 98, 1987

Haring 11, Van Dis ML: Odontogenic keratocyst. a clinical radiographic and histopathologic study. Oral Surg Oral Med Oral Pathol 66:145, 1988

lrvine GH, Bowerman JE: Mandihular keratocysts: surgical management. Er J Oral Maxillofac Surg 23: 204,1985

Kamiya Y, Narita H, Yamamato T, et at: Familial odontogenic keratocysts. Int J Oral Surg 14:73, 1985

Larsen PE, Hegtvedt AK: Odontogenesis and odontogenic cysts and tumors. in: Otolaryngology Head and Neck Surgery. Cummings CW, Fredrickson JM, Harker LA, Krause CJ, Schuller DE ( eds ). St Louis, Moshy, 1992. p: 1414.

McLoughlin PM, Dickenson Al, Avery BS: Gorlin's syndrome and Van Reckling hausen's disease occurring in one family. Br J Oral Ma:xillofac Surg 29:189, 1991

Mustaciuolo VW, Brahney CP, Aria AA: Recurrent keratocysts in hasal cell nevus syndrome. review of the literature and report of a case. J Oral Maxillofac Surg 47: 870, 1989

Pindhorg JJ, Hansen J: Studies on odonto genic cyst epithelium ll. Clinical and roentgenographig aspects of odontogenic keratocysts. Acta Pathol Microbiol Scand 58:283, 1963

Woolgar JA, Rippin JW, Browne RM: The odontogenic keratocyst and its occurrence in the nevoid hasal cell carsinoma synd rome. Oral Surg Oral Med Oral Pathol 64:727, 1987

Woolgar JA, Rippin JW, Browne RM: A comparative histological study of odonto genic keratocysts in basa[ cell naevus syndrome and control patients. J Oral Pathol 16:75, 1987

Zachariades N, Papanikolau S, Trianta fyllou D: Odontogenic keratocysts: review of the literature and report of sixteen cases. J Oral Maxillofac Surg 43:177, 1985